FOP – 1

Sample questions.

1. A girl presents at 60 hours of age with lethargy, poor perfusion and jaundice. She is breast fed. Parents are Caucasian. Clinical examination reveals jaundice and liver edge just palpable below coastal margin.

Investigations

Maternal blood group:            A positive 

Baby blood group:                  O positive.

Direct Coombs test:                 Negative.

Total Bilirubin:                       444 (µmol/L).  (<300 µmol/L). 

Conjugated bilirubin:              17(µmol/L). ( <35µmol/L). 

Which is the most likely cause? Select one answer only.

a.  ABO incompatibility

b. Dehydration

c. Galactosaemic

d. G6PD deficiency

e. Septicaemia

2. Which of the following is not a clinical feature of Duchene Muscular dystrophy?

a. Delayed walking

b. Delayed speech

c. Defective vision

d. Constipation

e. Defective hearing

3. The following are poor prognostic feature of acute lymphoblastic leukaemia except:

a) Age less than 1 year

b) WBC >100 x 10 9  /l

c) Chromosome count >50

d) DNA index <1.16

e) M2 and M3 marrow

4. Darshan, a 10 year old male child, is noticed to be having sleep disturbances off late. He goes early to bed but starts making loud unusual noises once falling asleep. His mother has seen scary rowing eye ball movements during the episode. Next day he feels tiered but does not recollect the event. EEG shows high amplitude spikes in centrotemporal region.

Which of the following about his clinical condition is true?

  1. Needs lifelong anticonvulsants
  2. It may spontaneously resolve
  3. May have language regression
  4. May have defective vision
  5. It is hereditary

5. Mother of 5 yr old boy, a known diabetic, calls GP. He has history of loose tools and vomited two times overnight. He is drinking well. His GRBS (blood sugar) in the morning was 7 mmol/L (5-9 mmol/L).

What is the best management？

a)  continue same dose of insulin, increase sugary drinks and intake, monitor glucose and ketones

b) to reduce his insulin dose and give sugary drink。

c)  shift to hospital immediately

d) continue same dose and encourage oral intake 

e) reduce giving orally as child is vomiting。

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